Brain MRI Features in Horizontal Gaze Palsy with Progressive Scoliosis
Journal Title: Journal of Neuroimaging in Psychiatry and Neurology - Year 2017, Vol 2, Issue 1
Abstract
Horizontal gaze palsy with progressive scoliosis (HGPPS) is a rare disease with characteristic imaging features. We report a teenager girl with severe kyphoscoliosis and bilateral horizontal gaze palsy with normal other neurologic examination. The brain MRI revealed “tented” pons and “butterfly-shape” medulla. These changes are due to agenesis of deep structures of brainstem which play important roles in horizontal gaze and proprioception.
Authors and Affiliations
Mostafa Almasi, Mohammad Rohani, Atefeh Imani
Keywords
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- EP ID EP223593
- DOI 10.17756/jnpn.2017-012
- Views 142
- Downloads 0
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