Hirayama Disease: A Rare Neurological Entity
Journal Title: Nepal Journal of Neuroscience - Year 2013, Vol 10, Issue 1
Abstract
muscular amyotrophy of distal upper limbs is a rare disease predominantly affecting the anterior horn cells of the cervical cord in young men. We report the diagnostic radiological findings of a case of Hirayama disease, a kind of cervical myelopathy caused by flexion movements of the neck. In flexion MR studies of cervical spine the striking and pathognomonic picture of anterior shifting of posterior dura at the lower cervical spinal canal is seen. In nonflexion studies asymmetric cord atrophy is seen especially at the lower cervical cord, which is highly suggestive of Hirayama disease. When suspected, a flexion MR study of cervical spine is to be done to prove this diagnosis.
Authors and Affiliations
Isha Dhungana Shrestha, MD, PhD
Keywords
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