LANGERHANS CELL HISTIOCYTOSIS WITH PULMONARY INVOLVEMENT IN AN INFANT – A CASE REPORT.
Journal Title: GJRA-Global Journal For Research Analysis - Year 2019, Vol 8, Issue 10
Abstract
Background:1Langerhans cell histiocytosis (LCH) is characterized by monoclonal proliferation and inltration of organs by Langerhans cell. Pulmonary involvement is common in young adults, but it is uncommon in children. Case summary: A 7 month old female child, presented with shortness of breath and multiple hypopigmented macules with verrucous lesions over scalp. HRCT was chest, showed tiny cysts with cavitatory nodules and nodules with reticulations, likely to represent LCH. Skin biopsy had inltrating epidermis s/o LCH, immunohistochemistry revealed CD1a positive. Hence the diagnosis of Multisystemic Langerhans cell histiocytosis with pulmonary involvement was made. Infant planned to start chemotherapy but deteriorated, and succumbed to the disease. Conclusion: Pulmonary involvement is generally a component of systemic involvement. Therefore, children with persistent respiratory problems should be carefully evaluated for rare entities like Pulmonary LCH.
Authors and Affiliations
Dr. Minal Wade, Rashmi Prajapati, Anupama Mauskar
Keywords
Related Articles
- EP ID EP658487
- DOI -
- Views 84
- Downloads 0
Marine Mollusk Fauna of Kastamonu and Sinop Provinces: A Compiled list of Black Sea Mollusks of Turkey
The study was carried out to determine Mollusca fauna of Kastamonu and Sinop coasts. A seasonal sampling procedure was performed in the area from a variety of biotops in 0-0.5 and 5m depths at 4 stations between July 200...
AIRWAY MANAGEMENT IN EXTENSIVE FACIAL BURNS- A CASE REPORT
Anesthetic management of burns of the head, neck, face and upper airway needs special precautions as establishing the airway provides challenges to the anesthesiologist. A 27 year old female presented with acute second d...
HOW FMCG MARKETERS CAN USHER IN POSITIVE CHANGES IN CONSUMER BEHAVIOUR TOWARDS PURCHASE OF FMCG PRODUCTS
Fast-moving consumer goods (FMCGs) are products that sell quickly and at a relatively low price. Examples include non-durable goods such as soft drinks, toiletries, and grocery items. The FMCG sector has been growing at...
ORGANIC FARMING – PROBLEMS AND PROSPECTS
The organic farming sector is suffering from a lot of problems such as insignificant growth. Organic Farmers find it difficult to continue their organic farming practices due to various reasons like inadequate support fr...
Interdisciplinary Mannequins with Moulage A Useful Labour Care Teaching Tool for Medical Graduate
Application of moulage to static mannequins, allows the learner improve their skills. Aim : To evaluate simulation-based teaching in labour care using mannequins . To assess confidence& competence after using simulators...