Multicentric Reticulohistiocytosis: A Rare Case Report
Journal Title: International Journal of Medical Research Professionals - Year 2017, Vol 3, Issue 6
Abstract
Multicentric reticulohistiocytosis (MRH) is a rare multisystem disorder of unknown etiology, characterized by erosive polyarthritis and papulonodular lesions on the skin, mucous membranes, and internal organs. There is no published data on incidence and prevalence of MRH. As MRH is a rare entity so modem of information is available only in the form of case reports. Although clinically it mimicks rheumatoid arthritis and psoriatric arthritis, its spectrum is aggressive and poses a diagnostic challenge for rheumatologists and dermatologists. Diagnosis is made clinically by the characteristics cutaneous and joint manifestations and is confirmed by typical histopathological appearance of non-Langerhans cell histiocytosis on skin biopsies. Prompt diagnosis and early treatment of this rare entity is vital as untreated cases can progress to severe destructive arthritis and disability.
Authors and Affiliations
Shushruta Mohanty, Aparajita Mishra, Pranati Mohanty, Kalpalata Tripathy
Keywords
Related Articles
- EP ID EP548834
- DOI 10.21276/ijmrp.2017.3.6.059
- Views 83
- Downloads 0
Livedoid Vasculopathy: A Case Report and Review of Literature
Livedoid Vasculopathy (LV) is a chronic vascular disorder due to vascular coagulopathies that is characterized by recurrent painful ulcers that usually involves the lower legs especially the ankles. Here in we report a c...
To Evaluate the Diagnostic Value of Various Procedures Like Endobronchial Biopsy, Bronchial Brushing, Bronchial Aspirate/Wash and Post Bronchoscopic Sputum Specimens in Diagnosis of Lung Malignancies
Background: Fiberoptic bronchoscopy has become an important diagnostic and therapeutic tool for management of chest diseases and has revolutionized practice of pulmonary medicine. Therefore it was planned to perform this...
Computed Tomographic Evaluation in Spine Trauma with Neurological Correlation in Thoracolumbar Burst Fractures
Introduction: Radiology plays a crucial role in the evaluation of a traumatized patient by providing information that allows timely and appropriate management of the patient. Plain radiography still remains the foundatio...
Awareness of Diabetic Patient Regarding Ocular Disease
Context: Raising the awareness about diabetes eye complications was shown to be vital for the early detection and management. In this study, we thought to assess the state of knowledge of diabetic patients about ocular d...
A Clinical Study to Evaluate Debridement Efficacy of Ultrasonic Irrigation Followed By Hand Rotary Instrumentation in Anterior Teeth
Introduction: Success of any endodontic treatment depends on proper preparation of the root canal space. Various factors responsible for achieving this success, such as reduction in the microbes and proper obturation of...