Orofacial Manifestations of Encephalotrigeminal Angiomatosis: A Case Report and Review of Literature
Journal Title: Indian Journal of Dental Advancements - Year 2017, Vol 9, Issue 4
Abstract
Sturge–Weber syndrome (SWS), also called as encephalotrigeminal angiomatosis, is a sporadically occurring neurocutaneous syndrome caused by persistence of transitory primordial arteriovenous connection of the fetal intracranial vasculature. It is characterized by vascular malformation with capillary venous angiomas that involve face, choroid of eye, and leptomeninges with resulting neurological and orbital manifestations. The diagnosis is usually considered in a child presenting with seizures and facial capillary malformation along the trigeminal nerve distribution. In this article, a case of SWS associated with oral manifestations and review on literature is presented.
Authors and Affiliations
Bhavana V, Balaji Babu B, Shilpa Rao J, Mounika Reddy M
Keywords
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- EP ID EP471918
- DOI 10.5866/2017.9.10226
- Views 76
- Downloads 0
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