Plexiform Neurofibroma of Scalp in a Child: A Case Report
Journal Title: Journal of Neurological Sciences-Turkish - Year 2012, Vol 29, Issue 3
Abstract
Epicranial neurofibromatosis is a rare diagnosis in Neurofibromatosis patients, frequently seen in the occipital region, which can be the cause of bone destruction. Although plexiform neurofibromas are congenital lesions, they have a risk of malignant transformation. Total excision is recommended at the time of diagnosis. They can be found out just after birth and in some cases none of neurofibromatosis signs exist. Physician should differentiate this high vascular tumor from other benign lesions of scalp. In this case report, a 10- year- old boy having progressively enlarging and painful right occipital mass was presented. The patient was operated successfully and the pathology was plexiform neurofibroma.
Authors and Affiliations
Mehmet Onal, Erdinc Civelek, Hakan Yakupoglu, Atilla Kircelli, Ebru Demiralay, Serhat Aygun
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