Plexiform Neurofibroma of the Larynx in Children: About an Unusual Case Report
Journal Title: Archives of Otolaryngology and Rhinology - Year 2016, Vol 2, Issue 2
Abstract
Introduction: The plexiform neurofibroma is a rare benign tumor which is often associated to type 1 neurofibromatosis or Von Recklinghausen’s disease. The laryngeal involvement in neurofibromatosis is extremely rare. The objective of our report is the consideration of laryngeal neurofibromatosis in the differential diagnosis of dyspnea in infants and children. Summary of the clinical case: We report the case of a 4 year-old child who presented with inspiratory dyspnea. Laryngoscopy revealed a mass obstructing completely the laryngeal vestibule. Pathological examination of the resected tissue revealed a plexiform neurofibroma after immunohistochemical examination. The patient had regular follow up and she remained symptom free. Discussion: There is an association between neurofibromatosis type 1 and plexiform neurofibromas of the larynx. Analysis of the margins of neurofibromas of the larynx associated with neurofibromatosis type 1 may help predict clinical behavior.
Authors and Affiliations
Mahdoufi R, Barhmi I, Tazi N, Sami R, Abada R, Roubal M, Mahtar M
Keywords
Related Articles
- EP ID EP352058
- DOI 10.17352/2455-1759.000020
- Views 74
- Downloads 0
The Effectiveness of Rehabilitation Programs of Learning Disabilities on Children with Attention Deficit Hyperactivity Disorder
Objective: The aim of this work is to evaluate the role of rehabilitation programs of learning disabilities on children with attention deficit hyperactivity disorder (ADHD) children, and compare the effect of pharmacolog...
Sudden Sensorineural Hearing Loss in patient with Chronic Myelogenous Leukemia – A case study
Rapid progressive sensorineural hearing damage as the early sign of a hematological illness is often found in patients with Chronic Myeloid Leukemia. A 100-year- old man presented to our outpatient department with 2 hour...
Stylohyoid Syndrome and its Surgical Treatment – A Case Report and Review of the Literature
Stylohyoid syndrome or eagle’s syndrome is caused by calcification of the stylohyoid ligament or elongation of the bony styloid process. It may remain asymptomatic or it may present with facial neuralgia, foreign body se...
Aggressive Thyroid Gland Carcinoma: A Case Series
In 2017 there were approximately 62000 new cases of thyroid cancer (TC) in the United States, with a death toll of less than 5%. This relatively low mortality rate is based on a grouping of all TC subtypes, which masks t...
Management of Cleft Lip and Palate: A Five Year Review
Introduction: Clefts of the lip may cause cosmetic and social problems. Clefts of the palate may affect feeding, speech and hearing. Objective: To document the clinical and epidemiological features, surgical techniques (...