Pulmonary hypertension associated with systemic sclerosis
Journal Title: Postępy Nauk Medycznych - Year 2012, Vol 25, Issue 2
Abstract
Pulmonary hypertension is currently one of the most severe organ complications and together with interstitial lung disease is the main cause of death of systemic sclerosis patients. Pulmonary hypertension in patients with systemic sclerosis developes due to obturatory angiopathy of the pulmonary arteries (isolated arterial pulmonary hypertension) or due to other organ manifestations (interstitial lung disease, disorders of the left part of the heart, venous-occlusive disease of the lungs or thrombotic complications). A significant progress in pharmacotherapy of pulmonary arterial hypertension has been made in the last two decades. Less is known about medication of secondary pulmonary hypertension such as in patients with interstitial lung disease or the left heart disease). Early diagnosis (due to screening examination) and proper differential diagnosis of pulmonary hypertension causes are key factors in administration of optimal management. It is also important to provide interdisciplinary care to the patients including that of rheumatologist, cardiologist, pulmonologist and rehabilitant.
Authors and Affiliations
Otylia Kowal-Bielecka, Żaneta Smoleńska
Keywords
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