Spontaneous Haemomediastinum and Fatal Haemoperitoneum in woman with Vascular Ehlers-Danlos Syndrome
Journal Title: Archives of Pulmonology and Respiratory Care - Year 2017, Vol 3, Issue 2
Abstract
Vascular Ehlers-Danlos Syndrome (EDS) presents with fragility of blood vessels, with high incidence of fatal hemorrhages in middle-age adults. We present a 38-year old female with vascular EDS presented to the emergency unit with spontaneous hemomediastinum and hemothorax. A selective arteriography showed a bronchial artery aneurysm that could be embolized. Coagulated hemothorax was cleared up using intrapleural instillation of urokinase. Acute massive hemoperitoneum happened a few hours later, due to spontaneous disruption of a splenic artery aneurysm. It could not be managed and led to the decease of the patient. Multifocal bleeding is a frequent threatening event in vascular EDS.
Authors and Affiliations
Cal Isabel, Fernández Elena, Méndez Jose V, Jarabo Jose R
Travelling to High Altitudes Could be Thrombogenetic!
People ascending to high altitude regions are at risk for a variety of health problems, commonly including acute mountain sickness (AMS), high-altitude cerebral oedema (HACE) and high-altitude pulmonary oedema (HAPE) etc...
Review of the literature about Thymic Carcinomas
Background: Thymic carcinomas (TC) are rare tumors with challenging diagnosis and management. We aimed to describe the clinical and microscopic characteristics of TC through a literature review. Results: 82 articles and...
Chronic Obstructive Pulmonary Disease and Occupational Exposures: Epidemiological Evidence from R. Macedonia
Introduction: The research found consistent associations between workplace exposures across a wide range of sectors and the development of chronic obstructive pulmonary disease (COPD) independently of or in concert with...
Placing Novel, Fixed-Dose Dual Bronchodilators within the nice Guidelines for Chronic Obstructive Pulmonary Disease -Reflections on the Past, Present and Future
The current National Institute for Health and Care Excellence (NICE) chronic obstructive pulmonary disease (COPD) guidelines were updated in 2010, reflecting clinical evidence available at that time. Since the guidelines...
Clinical and Functional Outcomes of Sensitizer-Induced Asthma in Bakers and Cotton Workers after Removal from Exposure
Introduction: Sensitizer-induced occupational asthma (OA) has significant health and socioeconomic outcomes in affected subjects. Objective: To evaluate clinical and functional outcomes of sensitizer-induced OA in baker...