Leri’s diseases – A rare mesenchymal sclerosing bone dysplasia of right femoral neck
Journal Title: INTERNATIONAL JOURNAL OF RECENT TRENDS IN SCIENCE AND TECHNOLOGY - Year 2016, Vol 20, Issue 3
Abstract
Introduction: Melorheostosis (synonyms: candle bone disease, melting wax syndrome, Leri disease) is a rare chronic bone disorder, first described in 1922 by Leri and Joanny. Men and women are equally affected, and no hereditary predilections have been discovered. Onset is insidious, and most common symptom is pain. Most common part of bone is diaphysis of the long bone of lower limb rarely the axial skeleton. Classical radiological appearance of ‘flowing hyperostosis’ resembles hardened wax that has dripped down the side of a candle. Here we described a case of Melorheostosis with characteristic clinical and imaging findings – a twenty five year old male presented to dept of orthopaedic; with complain of pain in the right leg and hip region which aggravated on vigorous exercise. Plain radiograph and CT shows hyperostotic areas with undulating irregular margin with evidence of irregular cortical thickening along the long axis of neck of right femur which are said to resemble the melting wax dripping down the side of a candle and pathology to confirm the diagnosis.
Authors and Affiliations
Ankit Jain, Ishita Gupta, Hemant Kumar Mishra, A P Verma
Keywords
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