Orthodontic treatment as part of complex care in a patient with Prader-Willi syndrome. Case report

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Orthodontic treatment as part of complex care in a patient with Prader-Willi syndrome. Case report

Journal Title: Forum Ortodontyczne - Year 2018, Vol 14, Issue 1

Abstract

Hopkins in 1861 was the first one to describe Prader-Willi syndrome, followed by Down in 1865. In 1956 Prader, Labhart and Willi described a hereditary form of obesity. This syndrome is a rare hereditary multi-systemic disorder. Aim. The aim of the paper was to present a case of a 13-year-old female patient with Prader-Willi syndrome treated at the Department of Orthodontics, Medical University of Warsaw. Case report. On admission a clinical examination was performed and medical history was taken. The following general symptoms were observed: facial dysmorphia, scoliosis, hypopigmentation, hypogonadism, hypersensitivity to light and sounds, and problems with thermoregulation. The patient was eligible for orthodontic treatment because she was diagnosed with a malocclusion. Conclusions. Patient’s multispeciality treatment plays a key role in treatment of Prader-Willi syndrome, and it should include: paediatric, endocrine, psychiatric treatment, muscle rehabilitation and orthodontic treatment, and with an early and appropriate diagnosis such management may bring extremely favourable outcomes. (Widmańska- Grzywaczewska A, Sobieska E, Zadurska M. Orthodontic treatment as part of complex care in a patient with Prader-Willi syndrome. Case report. Orthod Forum 2018; 14: 73-80)<br/><br/>

Authors and Affiliations

Anna Widmańska-Grzywaczewska, Ewa Sobieska, Małgorzata Zadurska

Keywords

Prader-Willi syndrome PWS diagnostics orthodontic treatment

EP ID EP346354
DOI 10.5604/01.3001.0012.0545
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